Medical Centre of Obstetrics-Gynecology and Sexology;
A birth defect, the MRKH syndrome type 1 is characterized by uterine and vaginal agenesis.
It is the case of a patient aged 21 that had no uterus and the vagina had 5cm in the lower part, without any upper part, within the uterine and vaginal agenesis.
MRKH syndrome type 2, aside of the lack of uterus and vagina, indicates other defects, too, the most frequently affecting the kidneys, as in this case.
Abnormalities appear also in the morphophysiology of labia, in which the labia majora are hypotrophic and difficult to see, having an erotic sensitivity much under that of the labia minora, which are hypertrophic and have neurovascular and anatomic direct ties to the clitoris.
As well, also within the particulars, the vaginal introitus is small in size and determines difficult penetration and copulation, by the different defective structures of the vagina.
The short vagina (5cm in length) in its lower side, given its connections to the hyper-eroticism area located behind the pubis, and particularly to the clitoris, but to the other erotic areas, too, as well as the inner sides of the labia minora, determined strong sexual arousal to the patient, which allowed the penetration of the vaginal introitus and copulation, within reasonable limits, but after the intercourse’s completion (orgasm and ejaculation), given that the pleasurable sensation disappeared, the patient began completely feeling local pain and bleeding, which made her rush into the hospital.
Muller agenesis, MRKH syndrome, partial vaginal aplasia, unilateral renal agenesis, urogenital folds